Hammersmith Functional Motor Scale for Spinal Muscular Atrophy (HFMS)
Click the buttons provided below to view information contained in a specific part of this record:
|
General Information
|
| Objectives |
|
A functional motor scale for use in children with spinal muscular atrophy type 2 and 3, in particular those with limited mobility, to give objective information on motor ability and clinical progression.
|
|
| Category of Outcome Measure |
|
| Disease Type |
| |
Used |
Validated |
| Anterior Horn Cell Disease |
|
X |
|
|
| Chronology of Development |
|
The HFMS is based loosely on a functional scale developed for boys with Duchenne Muscular Dystrophy (Scott & Hyde 1982) which, as a scale, was not a reliable indicator of change in weaker children. For this reason this particular scale was developed. Activities included in the scale were: rolling, sitting, lifting head from prone and supine, getting up from lying, propping on arms, 4 point kneeling, crawling, standing and stepping. An initial study determined that these items were achieved in normal infants more than 29 months of age and a second phase of the study performed the test 120 times on 58 patients with SMA. This resulted in the test items being ordered in terms of difficulty to gain a measure of grading for SMA.
|
|
| Time to Complete |
|
10 to 15 minutes with a co-operative child
|
|
| Mode of Assessment |
Administered by trained evaluator
|
|
| Age Group |
Children (2 to 11 Years)
Adolescents (12 to 15 Years)
|
|
| Age Related Limitations |
|
Applies to children greater than 29 months old.
|
|
| Languages |
| |
Original |
Definitive Validated Translation |
Informal Translation |
| English UK |
X |
|
|
| Italian |
|
|
X |
|
|
| Conditions of Use and Contact Information |
| Postal Address |
|
Great Ormond Steet Hospital for Children NHS Trust
Great Ormond Street, London, WC1N 3TH
|
|
| Phone |
|
00 44 (0) 2074059200 ext 0099
|
|
|
|
|
Questionnaire/Scale
|
| Domain Name / Number of Items |
|
| Additional Format Information |
|
|
| Question Types and Usage |
|
Each item scores 0 - 2 with 0 usually meaning unable, 1 meaning some adaptation and 2 meaning fully able. Details for each item are on the score sheet
|
|
| Total Score |
Yes - total score is calculated.
|
|
| Total Score - Range/Direction |
|
0 - 40, 40 being the highest score
|
|
| Sub-Score |
No - sub-score is not calculated.
|
|
| Sub-Score Range/Direction |
|
|
|
|
Reference 1
|
| Reference Details |
|
Main M.; Kairon H.; Mercuri E.; et al (2003) The Hammersmith Functional Motor Scale for Children with Spinal Muscular Atrophy: A Scale to Test ability and monitor progress in children with limited ambulation, European Journal of Paediatric Neurology, Vol 7, pp 155-159, Elsevier
|
|
| Other Information |
|
Article gives details of the scoring items.
|
|
|
|
|
Reference 2
|
| Reference Details |
|
Mercuri E.; Messina S.; Battini R.; et al (2006) Reliability of the Hammersmith functional motor scale for spinal muscular atrophy in a multicentric study, Neuromuscular Disorders, Vol 16, 93-98, Pergamon
|
|
| Other Information |
|
Article examines inter-observer reliability of the scale and stabiliy of the scale over time in a cohort of 90 non-ambulant children with type 2 or 3 SMA.
|
|
|
|
|
Reference 3
|
| Reference Details |
|
Kroschell K.; Maczulski J.; Crawford T.; et al (2006) A modified Hammersmith functional motor scale for use in mult-center resrach on spinal muscular atrophy, Neuromuscular Disorders, Vol 16, pp 417-426, Pergamon
|
|
| Other Information |
|
This modified version of the original scale reordered the items to make administration easier and defined items on the scale.
|
|
|
|
|
Reference 4
|
| Reference Details |
|
Hammersmith Functional Motor Scale for SMA (HFMS)
|
|
|
|
|
Reference 5
|
| Reference Details |
|
2009 Hammersmith Functional Motor Scale for SMA Manual (HFMS Manual)
|
|
|
|
