Inclusion Body Myositis Functional Rating Scale (IBMFRS)

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Developmental Status
Developmental Status of OM
Complete: In Use
More Information About Developmental Status
Unknown
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General Information
Background
Author/s or Creator/s
Unknown
Objectives
To assess function in patients with IBM.
Category of Outcome Measure
Functional
 
Disease Type
  Used Validated
Muscle X  
Chronology of Development
Jackson et al elected to modify the ALSFRS in order to develop a disease-specific instrument for IBM on the basis of similarities between IBM and ALS. Questions in the ALSFRS that they thought did not apply to IBM were substituted with new questions,and other questions were modified to be more applicable.
Time Information
Time to Recall
At Assessment
Recall Period
Not Applicable
Time to Complete
40 minutes
Application
Mode of Assessment
Self administered on site
Self administered off site
 
Age Group
Adults (16 Years and Over)
 
Age Related Limitations
Not Applicable
Languages
  Original Definitive Validated Translation Informal Translation
English US X    
Conditions of Use and Contact Information
Conditions of Use
Free Access
 
Copyright Owner
Unknown
Contact Name
Unknown
Organisation Name
Unknown
Postal Address
Unknown
URL (Web Address)
Unknown
Email Address
Unknown
Phone
Unknown
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Questionnaire/Scale
Domain Details
Number of Domains
10
Domain Name / Number of Items
Swallowing (1)
Handwriting (1)
Cutting Food and Handling Utensils (1)
Fine Motor Taks (1)
Dressing (1)
Hygiene (1)
Turning in Bed and Adjusting Covers (1)
Sit to Stand (1)
Walking (1)
Climbing Stairs (1)
Total Number of Items
10
Additional Format Information
Not Applicable
Equipment
Equipment Required
Pen and Paper
Equipment Description
Not Applicable
Response Details
Question Types and Usage
Multiple Choice
Scoring
Total Score
Yes - total score is calculated.
Total Score - Range/Direction
0 (worse) to 40 (better)
Sub-Score
Unknown
Sub-Score Range/Direction
Unknown
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Reference 1
Type of Reference
Key Reference
Reference Details
Jackson CE, Barohn RJ, Gronseth G, Pandya S, Herbelin L; Muscle Study Group.; (2008) Inclusion body myositis functional rating scale: a reliable and valid measure of disease severity; Muscle Nerve; Apr; Vol. 37; Iss. 4; pp 473-6
Web Address (URL)
http://www.ncbi.nlm.nih.gov/pubmed/18236463
Reference File ID
Not Applicable
Other Information
This paper contains the IBM FRS and details validation results based upon 28 IBM patients who completed the IBMFRS at baseline and monthly for 6 months during an trial of beta interferon. The IBMFRS showed statistically significant correlations (P  0.001) with maximal voluntary isometric contraction, manual muscle testing, handgrip dynamometry, and the amyotrophic lateral sclerosis (ALS) functional rating scale (ALSPRS). Compared to these other outcome measures, the IBMFRS was also the most sensitive measure of change over the course of the study.